Crouzon Syndrome

Crouzon syndrome is a genetic disorder known as a branchial arch syndrome. Specifically, this syndrome affects the first branchial (or pharyngeal) arch, which is the precursor of the maxilla and mandible. Since the branchial arches are important developmental features in a growing embryo, disturbances in their development create lasting and widespread effects. (adapted from Wikipedia)

Image from Pankajradio.blogspot (link)

This is an AP and lateral radiograph  of a 12 year old child who presented  Crouzon Syndrome post operative following VP Shunt for reduction of Hydrocephalus.  Hydrocephalus is common in crouzon syndrome because of Venous congestion.

 

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